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DeCS
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Descriptor English:
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Polyendocrinopathies, Autoimmune
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Descriptor Spanish:
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Poliendocrinopatías Autoinmunes
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Descriptor Portuguese:
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Poliendocrinopatias Autoimunes
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Synonyms English:
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AIRE Deficiency
APECED
APS Type 1
Autoimmune Polyendocrine Syndrome, Type 2
Autoimmune Polyendocrine Syndrome, Type II
Autoimmune Polyendocrinopathy Syndrome Type 1
Autoimmune Polyendocrinopathy with Candidiasis and Ectodermal Dystrophy
Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal Dystrophy
Autoimmune Polyglandular Syndrome Type I
Autoimmune Polyglandular Syndrome Type II
Autoimmune Polyglandular Syndrome Type III
Autoimmune Polyglandular Syndrome, Type 1
Autoimmune Polyglandular Syndrome, Type 3
Autoimmune Polyglandular Syndrome, Type I
Autoimmune Syndrome Type III, Polyglandular
Diabetes Mellitus, Addison Disease, Myxedema
Diabetes Mellitus, Addison's Disease, Myxedema
Multiple Endocrine Deficiency Syndrome, Type 2
Polyendocrine Autoimmune Syndrome, Type II
Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy, Autoimmune
Polyglandular Autoimmune Syndrome, Type 1
Polyglandular Autoimmune Syndrome, Type 2
Polyglandular Autoimmune Syndrome, Type 3
Polyglandular Autoimmune Syndrome, Type I
Polyglandular Deficiency Syndrome, Type 2
Polyglandular Type III Autoimmune Syndrome
Schmidt Syndrome
AIRE Deficiencies
Autoimmune Polyendocrinopathy
Autoimmune Polyendocrinopathy Candidiasis Ectodermal Dystrophy
Deficiency, AIRE
Polyendocrinopathy Candidiasis Ectodermal Dystrophy, Autoimmune
Polyendocrinopathy, Autoimmune
Polyendocrinopathy-Candidiasis-Ectodermal Dystrophy, Autoimmune
Syndrome, Schmidt
Syndrome, Schmidt's
Autoimmune Polyendocrinopathy-Candidiasis-Ectodermal-Dystrophy
Autoimmune Syndrome Type I, Polyglandular
Autoimmune Syndrome Type II, Polyglandular
Polyglandular Type I Autoimmune Syndrome
Polyglandular Type II Autoimmune Syndrome
Schmidt's Syndrome
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Tree Number:
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C19.787
C20.111.750
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Definition English:
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Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present. |
Indexing Annotation English:
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do not coordinate with specific endocrine disease term or CANDIDIASIS unless particularly discussed
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History Note English:
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1992
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Allowable Qualifiers English:
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Record Number:
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29879
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Unique Identifier:
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D016884
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Occurrence in VHL:
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Similar:
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DeCS CID-10 LILACS
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